Abstract

BACKGROUND:

Wilms' tumors (WT) most commonly occur between the ages of 2 and 5 years and are the second most common abdominal tumor in children, secondary to neuroblastomas(1).
It accounts for approximately 5–6% of the neoplasms in children and is rare in the adult population(2). Less than 3% of all the reported Wilms' tumor cases occur in adults. The overall survival of 83% has been recently reported with the use of primary nephrectomy followed by adjuvant combination chemotherapy(3).
Up to 4% of patients with WT have tumor thrombus involving the vena cava, and the incidence of cardiac involvement is about 0.8% to 1%(4,5). In adults, tumor extension into the vena cava and the right side of the heart is extremely rare.